Gastrosquise no Brasil em um Contexto Global

Autores

  • Virginia maria Muniz Universidade Federal do Espírito Santo
  • Lima bNúcleo de Terapia Intensiva Pediátrica e Neonatologia, Hospital Estadual Infantil Nossa Senhora da Glória, Vitória - ES, Brasil.
  • Luciane Bresciani Salaroli cDepartamento de Educação Integrada à Saúde, Programa de Pós-Graduação em Saúde Coletiva, Universidade Federal do Espírito Santo (UFES), Vitória, Espírito Santo, Brasil.
  • Eliana Zandonade dDepartamento de Estatística, Programa de Pós-Graduação em Saúde Coletiva, Universidade Federal do Espírito Santo, Vitória, Espírito Santo, Brasil.

DOI:

https://doi.org/10.36311/jhgd.v32.11796

Palavras-chave:

Brasil, anomalias congênitas, gastrosquise, recém-nascido, resultado da gravidez

Resumo

Introdução: a disparidade global nos resultados da gastrosquise é visível. Taxas de sobrevivência em países de alta renda melhoraram desde 1960 e atualmente estão em torno de 100%, devido ao progresso da cirurgia pediátrica e da terapia intensiva neonatal. No entanto, em países de media e baixa renda, as taxas de mortalidade continual elevadas.

Objetivo: este estudo tem como objetivo mapear a literatura existente sobre gastrosquise no Brasil e discutir as evidências disponíveis em um contexto global.

Método: revisão de escopo. Foram pesquisados o PubMed, o Scielo Brasil, a Biblioteca Virtual em Saúde (BVS) e o Google Scholar no período de janeiro de 2000 a maio de 2020.

Resultados: oito estudos preencheram os critérios de inclusão e os dados encontrados de 912 pacientes foram: idade materna média de 20.7 anos, média do diagnóstico antenatal de 80.2%, taxa média de cesarianas de 77.7%, tempo de permanência hospitalar médio de 40.8 dias e taxa média de mortalidade 25.3%. Os fatores de risco associados ao óbito encontrados foram a prematuridade, baixo peso ao nascer, APGAR baixo, reintervenções cirúrgicas, sepse, intervalo nascimento-cirurgia maior que 4 horas, poucas consultas do pré-natal e diagnóstico antenatal tardio.

Conclusão: estudos sobre gastrosquise no Brasil são escassos, a maioria realizada no Sudeste do país. Os piores desfechos estão em regiões com poucos recursos econômicos, situação semelhante à encontrada na literatura internacional. Esta revisão deve ser validada com estudos futuros que investiguem a situação de gestantes portadoras de fetos com gastrosquise, especialmente em regiões de poucos recursos, no Brasil.

Referências

Ruschkowsk B, Lafreniere A, Demellawy DE, Grynspan D. Gastroschisis Is Associated With Placental Delayed Villous Maturation. Pediatr Dev Pathol [Internet]. 2020 Sep [cited 2021 Aug 12]; 23(3): 197-203. Available from: https://journals.sagepub.com/doi/10.1177/1093526619875877

Opitz JM, Feldkamp ML, Botto LD. An evolutionary and developmental biology approach to gastroschisis. Birth Defects Res [Internet]. 2019 Fev [cited 2021 Aug 12]; 111(6): 294-311. Available from: https://onlinelibrary.wiley.com/doi/10.1002/bdr2.1481

Wright NJ, Sekabira JS, Ade-AJayi N. Care of infants with gastroschisis in low-resource settings. Semin Pediatr Surg [Internet]. Sep 2018 [cited 2021 Aug 12]; 27(5): 321-326. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7116007/

World Bank.Washington (DC): World Bank Country and Lending Groups [Internet]. 2019 [cited 2019 Dec 20]. Available from: https://datahelpdesk.worldbank.org/knowledgebase/articles/906519-world-bank-country-and-lending-groups

Instituto de Pesquisa Econômica Aplicada (IPEA) Brazilia: Radar IDHM: evolução do IDHM e de seus índices componentes no período de 2012 a 2017, 2019 [Internet]. 2019 [cited 2021 Aug 12] Available from: https://www.ipea.gov.br/portal/images/stories/PDFs/livros/livros/190416_rada_IDHM.pdf

Oliveira GS, Lima MCBM, Lyra CO, Oliveira AGRC, Ferreira MAF. Desigualdade espacial da mortalidade neonatal no Brasil: 2006 a 2010. Cien Saude Colet [Internet]. Aug 2013 [cited 2021 Aug 12]; 18(8): 2431-2441. Available from: https://www.scielo.br/j/csc/a/NMCvfFKCnkp5tHKjcHcHbfk/?lang=pt

Arksey H, O’Malley L. Scoping studies: towards a methodological framework. Int J Soc Res Methodol [Internet]. Feb 2007 [cited 2021 Aug 12]; 8(1): 19-32. Available from: https://www.tandfonline.com/doi/abs/10.1080/1364557032000119616

Levac D, Colquhoun H, O’Brien KK. Scoping studies: advancing the methodology. Implement Sci [Internet]. Sep 2010 [cited 2021 Aug 12]; 5:69. Available from: https://implementationscience.biomedcentral.com/articles/10.1186/1748-5908-5-69

Tricco AC, Lillie E, Zarin W, O’Brien KK, Colquhoun H, Levac D, et al. Extension for scoping reviews (PRISMA-ScR): checklist and explanation. Ann Intern Med [Internet]. Oct 2018 [cited 2021 Aug 12]; 169(7): 467-473.Available from: https://www.acpjournals.org/doi/full/10.7326/M18-0850?rfr_dat=cr_pub++0pubmed&url_ver=Z39.88-2003&rfr_id=ori%3Arid%3Acrossref.org

Bergholz R, Boettcher M, Reinshagen K, Wenke K. Complex gastroschisis is a different entity to simple gastroschisis affecting morbidity and mortality—A systematic review and meta-analysis. J Pediatr Surg [Internet]. Sep 2014 [cited 2021 Aug 12]; 49(10): 1527–32. Available from: https://www.jpedsurg.org/article/S0022-3468(14)00482-5/fulltext

Martins BMR, Abreu I, Méio MDB, Moreira MEL. Gastroschisis in the neonatal period: a prospective case-series in a Brazilian referral center. J Pediatr Surg [Internet]. Aug 2020 [cited 2021 Aug 12]; 55(8): 1546-1551. Available from: https://www.sciencedirect.com/science/article/abs/pii/S0022346820302943

Bilibio JP, Beltrão AM, Vargens AC, Gama TB, Lorenzzoni PL. Gastroschisis during gestation: prognostic factors of neonatal mortality from prenatal care to postsurgery. Eur J Obstet Gynecol Reprod Biol [Internet] Apr 2019 [cited 2021 Aug 12]; 237: 79-84. Available from: https://www.ejog.org/article/S0301-2115(19)30179-4/fulltext

Osmundo Jr GS, Mohamed SHM, Nishie EN, Tannuri ACA, Gibellia MABC, Francisco RPV, et al. Association of spontaneous labor onset with neonatal outcomes in pregnancies with fetal gastroschisis: A retrospective cohort analysis. Acta Obstet Gynecol Scand [Internet]. Feb 2019 [cited 2021 Aug 12]; 98(2): 154-161. Available from: https://obgyn.onlinelibrary.wiley.com/doi/10.1111/aogs.13473

Miranda ME, Emil S, Paixão RM, Piçarro C, Cruzeiro PCF, Campos BA, et al. A 25-year study of gastroschisis outcomes in a middle-income country. J Pediatr Surg [Internet]. Mar 2019 [cited 2021 Aug 12]; 54(7): 1481-1486. Available from: https://www.jpedsurg.org/article/S0022-3468(19)30137-X/fulltext

Carvalho NS, Helfer MT, Serni PO, Terasaka OA, Boute T, Araujo Junior E, et al. Postnatal outcomes of infants with gastroschisis: a 5-year follow-up in a tertiary referral center in Brazil. J Matern Fetal Neonatal Med [Internet]. Mar 2015 [cited 2021 Aug 12]; 29(3): 418-422. Available from: https://www.tandfonline.com/doi/abs/10.3109/14767058.2014.1002764?journalCode=ijmf20

Calcagnotto H, Müller ALL, Leite JCL, Sanseverino MTV, Gomes KW, Magalhães JAA. Fatores associados à mortalidade em recém-nascidos com gastrosquise. Rev Bras Ginecol Obstet [Internet]. Dec 2013 [cited 2021 Aug 12]; 35(12): 549-53. Available from: https://www.scielo.br/j/rbgo/a/bf6tmZc3rg49rqynbBkVm3r/?lang=pt

Tannuri ACA, Sbragia L, Tannuri U, Silva LM, Leal AJG, Schmidt AFS, et al. Evolution of critically ill patients with gastroschisis from three tertiary centers. Clinics [Internet]. 2011 [cited 2021 Aug 12]; 66(1): 17-20. Available from: https://www.scielo.br/j/clin/a/WsKpdM7BNtF3jbBWXJrmbTg/?lang=en

Vilela PC, Amorim MMR, Falbo GH, Santos LC. Risk Factors for Adverse Outcome of Newborns With Gastroschisis in a Brazilian Hospital. J Pediatr Surg [Internet]. Apr 2001 [cited 2021 Aug 12]; 36(4): 559-564. Available from: https://www.jpedsurg.org/article/S0022-3468(01)69750-1/fulltext

Fernandes FCGM, Santos EGO, Barbosa IR. Age of first pregnancy in Brazil: data from the national health survey. J Hum Growth Dev [Internet]. 2019 [cited 2021 Aug 12]; 29(3): 304-312. Available from: https://revistas.marilia.unesp.br/index.php/jhgd/article/view/9523

Youssef F, Laberge JM, Puligandla P, Emil S, Canadian Pediatric Surgery Network (CAPSNet). Determinants of outcomes in patients with simple gastroschisis. J Pediatr Surg [Internet]. Feb 2017 [cited 2021 Aug 12]; 52(5): 710-714. Available from: https://www.jpedsurg.org/article/S0022-3468(17)30051-9/fulltext

Overcash RT, DeUgarte DA, Stephenson ML, Gutkin RM, Norton ME, Parmar S, et al. Factors associated with gastroschisis outcomes. Obstet Gynecol [Internet]. Sep 2014 [cited 2021 Aug 12]; 124(3): 551-557. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4147679/

Tosello B, Zahed M, Guimond F, Baumstarck K, Faure A, Michel F, et al. Management and Outcome Challenges in Newborns with Gastroschisis: A 6-year retrospective French study. J Matern Fetal Neonatal Med [Internet]. Dec 2017 [cited 2021 Aug 12]; 30(23): 2864-2870. Available from: https://www.tandfonline.com/doi/abs/10.1080/14767058.2016.1265935?journalCode=ijmf20

Raymond SL, Hawkins RB, St. Peter SD, Downard CD, Qureshi FG, Renaud E, et al. Predicting Morbidity and Mortality in Neonates Born With Gastroschisis. J Surg Res [Internet]. Jan 2020 [cited 2021 Aug 12]; 245: 217-224. Available from: https://www.journalofsurgicalresearch.com/article/S0022-4804(19)30559-1/fulltext

Wesonga AS, Fitzgerald TN, Kabuye R, Kirunda S, Langer M, Kakembo N, et al. Gastroschisis in Uganda: Opportunities for improved survival. J Pediatr Surg [Internet]. Aug 2016 [cited 2021 Aug 12]; 51(11): 1772-1777. Available from: https://www.jpedsurg.org/article/S0022-3468(16)30193-2/fulltext

Marshall Niles SG, Mitchell-Fearon K, Gill MI, DeSouza CJ, Fearon IC, Abel CA, et al. Mortality-related factors in gastroschisis a Jamaican perspective. J Pediatr Surg [Internet]. Apr 2017 [cited 2021 Aug 12]; 52(4): 530-533. Available from: https://www.jpedsurg.org/article/S0022-3468(16)30506-1/fulltext

Zalles-Vidal C, Peñarrieta-Daher A, Bracho-Blanchet E, Ibarra-Rios D, Dávila-Perez R, Villegas-Silva R, et al. A Gastroschisis bundle: effects of a quality improvement protocol on morbidity and mortality. J Pediatr Surg [Internet]. Nov 2018 [cited 2021 Aug 12]; 53(11): 2117-2122. Available from: https://www.jpedsurg.org/article/S0022-3468(18)30387-7/fulltext

Haddock C, Skarsgard ED. Understanding gastroschisis and its clinical management: where are we? Expert Rev Gastroenterol Hepatol [Internet]. Apr 2018 [cited 2021 Aug 12]; 12(4): 405-415. Available from: https://www.tandfonline.com/doi/abs/10.1080/17474124.2018.1438890?journalCode=ierh20

Ramires de Jesus G, Ramires de Jesus N, Peixoto-Filho FM, Lobato G. Caesarean rates in Brazil: what is involved? BJOG [Internet]. Apr 2015 [cited 2021 Aug 12]; 122(5): 606–609. Available from: https://obgyn.onlinelibrary.wiley.com/doi/10.1111/1471-0528.13119

Du L, Pan WH, Cai W, Wang J, Wu YM, Shi CR. Delivery room surgery: an applicable therapeutic strategy for gastroschisis in developing countries. World J Pediatr [Internet]. Fev 2014; 10(1): 69-73. Available from: https://link.springer.com/article/10.1007%2Fs12519-014-0455-3

O’Connell RV, Dotters-Katz SK, Kuller JA, Strauss RA. Gastroschisis: A review of management and outcomes. Obstet Gynecol Surv [Internet]. Sep 2016 [cited 2021 Aug 12]; 71(9): 537-544. Available from: https://journals.lww.com/obgynsurvey/Abstract/2016/09000/Gastroschisis__A_Review_of_Management_and_Outcomes.18.aspx

Bhatt P, Lekshminarayanan A, Donda K, Dapaah‑Siakwan F, Thakkar B, Parat S, et al. Trends in incidence and outcomes of gastroschisis in the United States: analysis of the national inpatient sample 2010-2014. Pediatr Surg Int [Internet] Sep 2018 [cited 2021 Aug 12]; 34(9): 919-929. Available from: https://link.springer.com/article/10.1007%2Fs00383-018-4308-3

Skarsgard ED. Management of gastroschisis. Curr Opin Pediatr [Internet] Jun 2016 [cited 2021 Aug 12]; 28(3): 363-369. Available from: https://journals.lww.com/co-pediatrics/Abstract/2016/06000/Management_of_gastroschisis.17.aspx

Apfeld JC, Wren SM, Macheka N, Mbuwayesango BA, Bruzoni M, Sylvester KG, et al. Infant, maternal, and geographic factors influencing gastroschisis related mortality in Zimbabwe. Surgery [Internet] Dec 2015 [cited 2021 Aug 12]; 158(6): 1475-1480. Available from: https://www.surgjournal.com/article/S0039-6060(15)00368-2/fulltext

Wesonga A, Situma M, Lakhoo K. Reducing gastroschisis mortality: a quality improvement initiative at a Ugandan pediatric surgery unit. World J Surg [Internet]. May 2020 [cited 2021 Aug 12]; 44(5): 1395-1399. Available from: https://link.springer.com/article/10.1007%2Fs00268-020-05373-w

Mota GAO, Shimizu GY, Lahoz ALC, Nicolau CM, Paula LCS, Maristela TCunha MT, Tanaka C. Motor performance evaluation of newborns with gastroschisis after surgical correction. J Hum Growth Dev [Internet]. 2021 [cited 2021 Aug 12]; 31(2): 217-223. Available from: https://revistas.marilia.unesp.br/index.php/jhgd/article/view/12225/7517

Allin BSR, Hall NJ, Ross AR, Marven SS, Kurinczuk JJ, Knight M, et al. Development of a gastroschisis core outcome set. Arch Dis Child Fetal Neonatal Ed [Internet]. Jan 2019 [cited 2021 Aug 12]; 104(1): F76-F82. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6762000/

Publicado

2022-01-31

Edição

Seção

ORIGINAL ARTICLES