The numerous denominations of the Brugada syndrome and proposal about how to put an end to an old controversy - a historical-critical perspective
DOI:
https://doi.org/10.7322/jhgd.v30.11118Palavras-chave:
Brugada syndrome, eponymous, nomenclature, electrocardiographic hallmarkResumo
Introdução: A Síndrome de Brugada (SB), em homenagem à sua descoberta como entidade independente pelos irmãos espanhóis / catalães Pedro e Josep Brugada, tem merecido inúmeras denominações derivadas principalmente da correlação genótipo /fenótipo clínico. O objetivo deste manuscrito é apresentar e analisar as nomenclaturas que esta intrigante e desafiadora síndrome recebeu nos últimos 28 anos. Também comparamos as principais características entre os casos do primeiro relato dos irmãos Brugada e um artigo de Martini e col. As nomenclaturas utilizadas por esses autores estão intimamente ligadas à SB, mas os casos (exceto um) apresentados no artigo de Martini e cols. não apresentam o padrão eletrocardiográfico de Brugada tipo 1, obrigatório para o diagnóstico da SB.
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Copyright (c) 2020 Joseane Elza Tonussi Mendes
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