Challenges in the surgical treatment of a 8-year old child living with Prune Belly syndrome: case report

Authors

  • Rodrigo Alexandre Trivilato a Universidade Federal de Goiás – Departamento de Urologia
  • Gabriela Dadalt a Universidade Federal de Goiás – Departamento de Urologia
  • Deborah Lima Assenço a Universidade Federal de Goiás – Departamento de Urologia
  • Débora Fernandes Barbalho a Universidade Federal de Goiás – Departamento de Urologia
  • Márcio Rodrigues Costa a Universidade Federal de Goiás – Departamento de Urologia
  • Nadin Chater a Universidade Federal de Goiás – Departamento de Urologia
  • Rodrigo Rosa Lima a Universidade Federal de Goiás – Departamento de Urologia
  • Bernardo Monteiro Antunes Barreira a Universidade Federal de Goiás – Departamento de Urologia
  • João Paulo de Bessa Teixeira a Universidade Federal de Goiás – Departamento de Urologia
  • Fernando Cruvinel a Universidade Federal de Goiás – Departamento de Urologia
  • José Luiz Figueiredo b Universidade Federal de Pernambuco Departamento de cirurgia

DOI:

https://doi.org/10.36311/jhgd.v33.13793

Keywords:

Prune Belly Syndrome, eagle-barrett syndrome, Monford abdominoplasty, case report

Abstract

Prune Belly syndrome, also known as Eagle-Barret syndrome, is a rare disease, with a prevalence of 3.8 live births per 100,000 births. Its main characteristic is the hypoplasia of the abdominal muscles, giving rise to the name “prune belly syndrome”. The gold standard treatment is surgery, ideally with correction of cryptorchidism and phimosis between 6 to 18 months of life. Correction of urinary malformations and abdominoplasty should be performed up to 4 years of age. Little evidence exists in the literature about late treatment and its implications for prognosis. The context mentioned above led us to present an uncommon case of a six years old child in which a surgical approach was performed later than usual.

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References

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Published

2023-03-23

Issue

Vol. 33 No. 1 (2023)

Section

ORIGINAL ARTICLES

License

Copyright (c) 2022 Trivilato RA, Dadalt G, Assenço DL, Barbalho DF, Costa MR, Chater N, Lima RR, Barreira BMA, Teixeira JPB, Cruvinel F, Figueiredo JL

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.