Gastroschisis in Brazil within a Global Context


  • Virginia maria Muniz aPrograma de Pós-Graduação em Saúde Coletiva. Universidade Federal do Espírito Santo (PPGSC/UFES), Vitória, Espírito Santo, Brasil.
  • Antônio Lima Netto bNúcleo de Terapia Intensiva Pediátrica e Neonatologia, Hospital Estadual Infantil Nossa Senhora da Glória, Vitória - ES, Brasil.
  • Luciane Bresciani Salaroli cDepartamento de Educação Integrada à Saúde, Programa de Pós-Graduação em Saúde Coletiva, Universidade Federal do Espírito Santo (UFES), Vitória, Espírito Santo, Brasil.
  • Eliana Zandonade dDepartamento de Estatística, Programa de Pós-Graduação em Saúde Coletiva, Universidade Federal do Espírito Santo, Vitória, Espírito Santo, Brasil.



Brazil, congenital abnormalities, gastroschisis, newborn, pregnancy outcomes


Introduction: global disparity in outcomes of gastroschisis is visible. Survival rates in high-income countries have improved since 1960, and are currently around 100%, due to progress in pediatric surgery and neonatal intensive care. However, in low- and middle-income countries mortality rates can reach all cases.

Objective: this study aims to map the existing literature on gastroschisis in Brazil within a global context.

Methods: scoping Review. PubMed, Scielo Brazil, Biblioteca Virtual em Saúde (BVS) and Google Scholar, were searched from January 2000 to May 2020.

Results: eight studies met the inclusion criteria. The consolidated data of 912 patients were: Mean maternal age of 20.7 years, antenatal diagnosis rate of 80.2%, cesarean section rate of 77.7%. Mean of hospital stay of 40.8 days. Mean mortality rate of 25.3 %. Risk factors associated with death were: prematurity, low birth weight, low APGAR score, reinterventions, sepsis, birth-to-surgery interval greater than 4 hours, fewer prenatal visits, delayed prenatal diagnosis.

Conclusion: studies on gastroschisis in Brazil were scarce, most of carried out in southeast of country. This study suggests that there are regional contrasts on gastroschisis outcomes in Brazil. The worst results are in regions with low economic resources, a similar situation found in international literature. This review should be validated with future studies to investigate the situation of pregnant women with fetuses with gastroschisis, especially in low-resource regions, in Brazil.


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